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Desmoplastic Infantile Astrocytoma and Ganglioglioma

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Abstract

Rare superficial cerebral cortical and leptomeningeal large cystic tumors with dural attachment primarily occurring in infants. Most patients are under 2 years of age. Account for 1.25% of all childhood brain tumors with a 1.5:1 male to female ratio. Characterized by neoplastic neuroepithelial cells in a desmoplastic stroma showing variable astrocytic differentiation [desmoplastic infantile astrocytoma, (DIA)] or combined astrocytic and neuronal differentiation [desmoplastic infantile ganglioglioma, (DIG)].

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Author information

Authors and Affiliations

  1. Section of Neuropathology and Molecular Neuropathology Laboratory, Department of Pathology, Texas Children’s Hospital, Baylor College of Medicine, Houston, TX, USA

    Adekunle M. Adesina M.D., Ph.D. (Professor of Pathology, Medical Director)

Authors
  1. Adekunle M. Adesina M.D., Ph.D.
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Editors and Affiliations

  1. Dept. Pathology, Baylor College of Medicine, Baylor Plaza 1, Houston, 77030, U.S.A.

    Adekunle M. Adesina

  2. School of Medicine, University of California, Parnassus Ave. 505, San Francisco, 94143, U.S.A.

    Tarik Tihan

  3. VCU Medical Center, Virginia Commonwealth University, E. Marshall Street 1200, Richmond, 23298, U.S.A.

    Christine E. Fuller

  4. Children's Hospital Boston, Harvard Medical School, Longwood Ave. 300, Boston, 02115, U.S.A.

    Tina Young Poussaint

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Adesina, A.M. (2010). Desmoplastic Infantile Astrocytoma and Ganglioglioma. In: Adesina, A., Tihan, T., Fuller, C., Poussaint, T. (eds) Atlas of Pediatric Brain Tumors. Springer, New York, NY. https://doi.org/10.1007/978-1-4419-1062-2_16

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  • DOI: https://doi.org/10.1007/978-1-4419-1062-2_16

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  • Publisher Name: Springer, New York, NY

  • Print ISBN: 978-1-4419-1061-5

  • Online ISBN: 978-1-4419-1062-2

  • eBook Packages: MedicineMedicine (R0)

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