Lymphedema pp 427-436 | Cite as

Primary Lymphedema and Klippel-Trénaunay Syndrome

  • Byung-Boong Lee
  • James Laredo
  • Richard F. Neville
  • Raul Mattassi


The majority of primary lymphedemas1,2 are due to a congenital, independent lesion of the lymphatic system resulting in dysfunction. Primary lymphedema due to a truncular lymphatic malformation (LM) has been thoroughly reviewed in Chap. 51.


Vascular Malformation Venous Malformation Venous Insufficiency Marginal Vein Chronic Venous Insufficiency 
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Copyright information

© Springer-Verlag London Limited 2011

Authors and Affiliations

  • Byung-Boong Lee
    • 1
  • James Laredo
  • Richard F. Neville
  • Raul Mattassi
  1. 1.Department of Surgery, Division of Vascular SurgeryGeorge Washington University School of MedicineWashingtonUSA

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