Lymphedema pp 419-426 | Cite as

Primary Lymphedema as a Truncular Lymphatic Malformation

  • Byung-Boong Lee
  • James Laredo
  • Richard F. Neville


Primary lymphedema has been treated successfully for many decades and is one of the two main types of chronic lymphedema; the other is secondary lymphedema.1,2 Primary and secondary lymphedema are two different diseases with different etiologies, clinical behavior, response to treatment, and prognosis. Throughout the last decade, substantial progress has been made in the understanding of the true nature of primary lymphedema as a type of congenital vascular malformation (CVM)3,4 affecting the lymphatic system.


Lymphatic System Venous Malformation Lymphatic Malformation Compression Therapy Chronic Lymphedema 
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Copyright information

© Springer-Verlag London Limited 2011

Authors and Affiliations

  • Byung-Boong Lee
    • 1
  • James Laredo
  • Richard F. Neville
  1. 1.Department of Surgery, Division of Vascular SurgeryGeorge Washington University School of MedicineWashingtonUSA

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