• Megan K. Dishop


Diffuse pulmonary lymphangiomatosis is a rare proliferative process involving pulmonary lymphatic channels, sometimes also involving adjacent mediastinal, retroperitoneal, and thoracic wall tissues. Lymphangiomatosis is typically a sporadic condition, without known familial or genetic predisposition. Age at presentation is most commonly in late childhood, but ranges from infancy to late adulthood. Diagnostic imaging shows diffuse interstitial infiltrates, thickened septal lines and fissures, pleural thickening, and pleural effusions.


Pleural Effusion Respir Crit Disseminate Intravascular Coagulation Late Adulthood Late Childhood 

Copyright information

© Springer Science+Business Media, LLC 2010

Authors and Affiliations

  • Megan K. Dishop
    • 1
  1. 1.Texas Children’s HospitalHoustonUSA

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