The aortic valve in these patients is most often myxomatous and bicuspid with a single, fused commissure and an eccentrically placed orifice, or unicuspid (dome-shaped). The valve annulus may be small for age, but there is evidence that following dilation even quite small annuli may grow to a normal or near normal dimension (1). Myxomatous valves may mature, as Myxomatous pulmonary valves. Because there is a spectrum to left-sided obstructive lesions, often the first decision in many of these patients is whether they should have a valvotomy or a staged one-ventricle repair.
KeywordsAortic Valve Mitral Valve Stenosis Pigtail Catheter Valve Annulus Retrograde Approach