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Cystic Fibrosis

  • Annick Clement
  • Harriet Corvol
  • Brigitte Fauroux
Part of the Molecular Pathology Library book series (MPLB, volume 1)

Abstract

Cystic fibrosis (CF) is the most common lethal inherited disease of Caucasians. It is a disease of exocrine gland function involving many tissues and leading to a diverse range of pathologic and clinical problems. Although most patients have multiple organ involvement, pulmonary disease is the principal cause of both morbidity and mortality in more than 90% of patients surviving the neonatal period.1,2

Keywords

Cystic Fibrosis Respir Crit Airway Surface Liquid Sweat Test CFTR Gene 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

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Copyright information

© Springer Science+Business Media, LLC. 2008

Authors and Affiliations

  • Annick Clement
    • 1
  • Harriet Corvol
    • 2
  • Brigitte Fauroux
    • 2
  1. 1.Pediatric Pulmonology DepartmentHopital d’enfants Armand TrousseauParisFrance
  2. 2.Department of Pediatric PulmonologyHopital d’enfants Armand TrousseauParisFrance

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