Unusual Benign and Malignant Neoplasms of Lung: Molecular Pathology
Pulmonary sclerosing hemangioma is a unique lung neoplasm. It occurs sporadically in middle-aged patients, although cases have been reported in the pediatric population and may be associated with familial adenomatous polyposis.1,2 Sclerosing hemangiomas are typically peripheral and involve lung parenchyma. However, they rarely present as endobronchial polypoid masses resulting in clinical symptoms of bronchial obstruction.3 The lesions have sclerosis and hemorrhagic cystic spaces lined by surface/cuboidal cells thought to be reactive and solid areas consisting of round/polygonal cells thought to be neoplastic. For many years sclerosing hemangioma was thought to be a vascular tumor because of its microscopic appearance, hence the name.
KeywordsTuberous Sclerosis Complex Glomus Tumor Myxoid Liposarcomas Sarcoma Alveolar Soft Part Cartilaginous Tumor
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