Also known as solid-cystic tumor, papillary-cystic tumor, and solid and papillary tumor of the pancreas, this low-grade primary pancreatic epithelial neoplasm accounts for 1% of all exocrine pancreatic neoplasms. It occurs predominantly in adolescent girls and young women and is rare in men and children. Patients often present with vague abdominal discomfort/pain and an enlarging abdominal mass. Not infrequently, patients are asymptomatic and the tumors are found incidentally on physical examination or by imaging for the workup for unrelated conditions. Jaundice and hormonal disturbances are rare. Ultrasound and computed tomography (CT) usually reveal a well-demarcated and variably cystic mass, averaging 10cm and usually located in the body or tail of the pancreas. Tumor calcification may be present. As smaller tumors are identified with the increased use of more sensitive imaging techniques, cystic degeneration and calcification are often not seen.
KeywordsIntraductal Papillary Mucinous Neoplasm Acinar Cell Carcinoma Pancreatic Endocrine Tumor Cystic Degeneration Necrotic Debris
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