• David C. Chhieng
  • Edward B. Stelow
Part of the Essentials in Cytopathology book series (EICP, volume 3)


Pancreatoblastoma is extremely rare and represents 0.5% of all pancreatic epithelial tumors. It primarily occurs in children 10 years of age or younger, although cases in adults have been reported. There is a slight male predominance. Patients usually present with an abdominal mass with or without nonspecific symptoms such as pain and weight loss. Jaundice is notably uncommon. About one third of patients have elevated serum levels of alpha-fetoprotein (AFP). Radiologic examination often reveals a well-de marcated, heterogeneous mass. Calcification is not unusual.


Pancreatic Ductal Adenocarcinoma Acinar Cell Carcinoma Stromal Component Pancreatic Endocrine Tumor Ancillary Study 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.


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Suggested Reading

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Copyright information

© Springer Science+Business Media, LLC 2007

Authors and Affiliations

  • David C. Chhieng
    • 1
  • Edward B. Stelow
    • 2
  1. 1.Department of PathologyUniversity of Alabama at BirminghamBirminghamUSA
  2. 2.Department of PathologyUniversity of VirginiaCharlottesvilleUSA

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