Pancreatoblastoma is extremely rare and represents 0.5% of all pancreatic epithelial tumors. It primarily occurs in children 10 years of age or younger, although cases in adults have been reported. There is a slight male predominance. Patients usually present with an abdominal mass with or without nonspecific symptoms such as pain and weight loss. Jaundice is notably uncommon. About one third of patients have elevated serum levels of alpha-fetoprotein (AFP). Radiologic examination often reveals a well-de marcated, heterogeneous mass. Calcification is not unusual.
KeywordsPancreatic Ductal Adenocarcinoma Acinar Cell Carcinoma Stromal Component Pancreatic Endocrine Tumor Ancillary Study
Unable to display preview. Download preview PDF.