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Granulomatous Slack Skin

Abstract

Granulomatous slack skin (GSS) is a subtle variant of mycosis fungoides that is easily overlooked on initial biopsy due to its well-formed granulomatous appearance (1). The initial clinical presentation is similar to that of conventional mycosis fungoides in that patients present with erythematous-to-violaceous patches and plaques. As the lesions progress, however, pendulous folds develop on flexural surfaces of extremities, especially the axillae and inguinal regions (Figure 3.1). Less commonly, the skin on the trunk is affected. At this point in the course of the disease, the clinical appearance is similar to that of cutis laxa. This extremely rare variant of mycosis fungoides affects middle-aged adults with a slight predilection for women in some, but not all, series (2–5). It is most common in Caucasians.

Keywords

Multinucleated Giant Cell Mycosis Fungoides Atypical Lymphocyte Initial Clinical Presentation Cutis Laxa 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

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© Springer Science+Business Media, LLC 2007

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