In this anomaly, the left coronary artery usually arises from the main pulmonary artery, usually resulting in left, ventricular and septal ischemia and development of extensive collaterals between the right and left coronary arteries. Surgical repair is performed at any age immediately following the establishment of the diagnosis. Early repair is performed to avoid congestive heart failure and myocardial fibrosis caused by inadequate myocardial perfusion accentuated by a steal phenomenon with retrograde flow from the left coronary into the main pulmonary artery. Surgery should always establish a two-coronary system.
KeywordsPulmonary Artery Cardiopulmonary Bypass Left Coronary Artery Main Pulmonary Artery Hypoplastic Left Heart Syndrome
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