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Clinical Medicine Research pp 131–138Cite as

Epidemiology of Granulomatosis with Polyangiitis in Poland, 2011–2015

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Part of the book series: Advances in Experimental Medicine and Biology ((CLEXBI,volume 1116 ))

Abstract

Granulomatosis with polyangiitis (GPA) is a form of vasculitis that affects small- and medium-sized vessels in many organs. The aim of the study was to describe the epidemiology of GPA in Poland in 2011–2015, including the incidence and prevalence rates. The authors conducted a retrospective, population-based study, using hospital discharge records with GPA diagnosis. GPA incidence was estimated on the basis of the data from the Polish hospital morbidity study carried out by the National Institute of Public Health. The final study group consisted of 1491 patients (749 females, 742 males) who were first time hospitalized with the diagnosis of GPA. The average annual incidence of GPA in Poland was 7.7/1,000,000 (95% CI, 4.1–11.4), and the point prevalence at the end of 2015 was 36/1,000,000. A statistically significant decrease in the GPA incidence was noticed in this study. A 1-year survival rate for GPA was 94%. In conclusion, the incidence and prevalence rates of GPA in Poland are similar to that reported in other European countries. The study provides recent epidemiological data on GPA in Poland, which may be useful for comparisons with other geographical regions.

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Conflicts of Interest

Authors declare no conflict of interest in relation to this article.

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Authors and Affiliations

  1. Department of Social Medicine and Public Health, Medical University of Warsaw, Warsaw, Poland

    Krzysztof Kanecki, Aneta Nitsch-Osuch, Patryk Tarka & Magdalena Bogdan

  2. National Institute of Public Health–National Institute of Hygiene, Warsaw, Poland

    Paweł Gorynski

  3. Institute of Rural Health in Lublin, Lublin, Poland

    Piotr Tyszko

Authors
  1. Krzysztof Kanecki
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  2. Aneta Nitsch-Osuch
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  3. Paweł Gorynski
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  4. Patryk Tarka
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  5. Magdalena Bogdan
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  6. Piotr Tyszko
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Corresponding author

Correspondence to Krzysztof Kanecki .

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Editors and Affiliations

  1. Opole Medical School, Opole, Poland

    Mieczyslaw Pokorski

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Kanecki, K., Nitsch-Osuch, A., Gorynski, P., Tarka, P., Bogdan, M., Tyszko, P. (2018). Epidemiology of Granulomatosis with Polyangiitis in Poland, 2011–2015. In: Pokorski, M. (eds) Clinical Medicine Research. Advances in Experimental Medicine and Biology(), vol 1116 . Springer, Cham. https://doi.org/10.1007/5584_2018_239

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