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Oncocytomas and Rare Renal Tumors

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Urological Cancers

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Summary

New tumor entities have been described, which are characteristic for children or young adults. The predominance of TFE translocation carcinomas in the first decades of life demonstrates that renal cell carcinomas in young patients contain genetically and phenotypically distinct tumors with further potential for novel renal cell carcinoma subtypes. The far lower frequency of clear cell carcinomas with VHL alterations in childhood compared to adults suggests that renal cell carcinomas in young patients have a unique genetic background.

Other tumors with apparent predilection for young age groups include clear cell carcinomas in the context of von Hippel-Lindau disease, carcinomas in combination with nephroblastomas, and renal cell carcinomas associated with neuroblastomas.

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Authors and Affiliations

  1. Institute for Surgical Pathology, Department Pathology, University Hospital, Zürich, Switzerland

    Holger Moch MD

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  1. Holger Moch MD
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Editor information

Editors and Affiliations

  1. Faculty of Medicine, Hammersmith Campus, Imperial College London, London, UK

    Jonathan Waxman BSc, MD, FRCP (Professor of Oncology) (Professor of Oncology)

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© 2005 Springer-Verlag London Limited

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Moch, H. (2005). Oncocytomas and Rare Renal Tumors. In: Waxman, J. (eds) Urological Cancers. Springer, London. https://doi.org/10.1007/1-84628-015-X_25

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  • DOI: https://doi.org/10.1007/1-84628-015-X_25

  • Publisher Name: Springer, London

  • Print ISBN: 978-1-85233-911-1

  • Online ISBN: 978-1-84628-015-3

  • eBook Packages: MedicineMedicine (R0)

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