Partial Anomalous Pulmonary Venous Connection (PAPVC)

  • In Sook Park
  • Hyun Woo Goo


This chapter includes definition, types, morphology, clinical manifestations, diagnosis, natural course, treatment, and fetal diagnosis of partial anomalous pulmonary venous connection and scimitar syndrome.


Scimitar syndrome 

Suggested Reading

  1. 1.
    DeLeon SY, Freeman JE, Ilbawi MN, et al. Surgical techniques in partial anomalous pulmonary veins to the superior vena cava. Ann Thorac Surg. 1993;55:1222–6.CrossRefGoogle Scholar
  2. 2.
    Dupuis C, Charaf LA, Breviere GM, Abou P. “Infantile” form of the scimitar syndrome with pulmonary hypertension. Am J Cardiol. 1993;71:1326–30.CrossRefGoogle Scholar
  3. 3.
    Gikonyo DK, Tandon R, Lucas RV Jr, Edwards JE. Scimitar syndrome in neonates: report of four cases and review of the literature. Pediatr Cardiol. 1986;6:193–7.CrossRefGoogle Scholar
  4. 4.
    Hoey ET, Lewis G, Yusuf S. Multidetector CT assessment of partial anomalous pulmonary venous return in association with sinus venosus type atrial septal defect. Quant Imaging Med Surg. 2014;4(5):433–4.PubMedPubMedCentralGoogle Scholar
  5. 5.
    Moore JW, Kirby WC, Rogers WM, Poth MA. Partial anomalous pulmonary venous drainage associated with 45, X Turner’s syndrome. Pediatrics. 1990;86:273–6.PubMedGoogle Scholar
  6. 6.
    Najm HK, Williams WG, Coles JG, Rebeyka IM, Freedom RM. Scimitar syndrome: twenty years’ experience and results of repair. J Thorac Cardiovasc Surg. 1996;112:1161–9.CrossRefGoogle Scholar
  7. 7.
    van Meter C Jr, LeBlanc JG, Culpepper WS III, Ochsner JL. Partial anomalous pulmonary venous return. Circulation. 1990;82(5 suppl):IV195–8.PubMedGoogle Scholar

Copyright information

© Springer Nature Singapore Pte Ltd. 2019

Authors and Affiliations

  • In Sook Park
    • 1
  • Hyun Woo Goo
    • 2
  1. 1.Department of Pediatric CardiologyUniversity of Ulsan College of Medicine, Asan Medical CenterSeoulSouth Korea
  2. 2.Department of RadiologyUniversity of Ulsan College of Medicine, Asan Medical CenterSeoulSouth Korea

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