Atrial Isomerism

  • In Sook Park
  • Hyun Woo Goo


This chapter includes morphology, clinical manifestations, diagnosis, natural and unnatural course, treatment, including Kawashima operation and Fontan operation, and fetal diagnosis of congenital heart disease typically associated with right and left (atrial) isomerism. Positional abnormalities of the heart and anomalies of noncardiac organs typically seen in atrial isomerism are also presented.


Asplenia syndrome Polysplenia syndrome Atrial appendage Common atrium Nonconfluent PA Bilateral ducti Sliding hernia IVC interruption Complete AV block 

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Copyright information

© Springer Nature Singapore Pte Ltd. 2019

Authors and Affiliations

  • In Sook Park
    • 1
  • Hyun Woo Goo
    • 2
  1. 1.Department of Pediatric CardiologyUniversity of Ulsan College of Medicine, Asan Medical CenterSeoulSouth Korea
  2. 2.Department of RadiologyUniversity of Ulsan College of Medicine, Asan Medical CenterSeoulSouth Korea

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