Ebstein’s Anomaly

  • In Sook Park
  • Soo-Jin Kim
  • Hyun Woo Goo


This chapter includes types, morphology, clinical manifestations, diagnosis, natural course, treatment, and fetal diagnosis of Ebstein’s anomaly, including functional pulmonary atresia.


Crux cordis Septal displacement 

Suggested Reading

  1. 1.
    Anderson HN, Dearani JA, Said SM, et al. Cone reconstruction in children with Ebstein anomaly: the Mayo Clinic experience. Congenit Heart Dis. 2014;9:266–71.CrossRefGoogle Scholar
  2. 2.
    Almeida-Filho OC, Schmidt A, Marin-Neto JA, Maciel BC. Functional pulmonary atresia in a newborn with normal intracardiac anatomy. Pediatr Cardiol. 2002;23:647–9.CrossRefGoogle Scholar
  3. 3.
    Carpentier A, Chauvaud S, Mace L, Relland J, et al. A new reconstructive operation for Ebstein’s anomaly of the tricuspid valve. J Thorac Cardiovasc Surg. 1988;96:92–101.PubMedGoogle Scholar
  4. 4.
    Cha MY, Won HS, Lee MY, et al. An unusual ultrasonographic manifestation of a fetal Ebstein anomaly. Obstet Gyneol Sci. 2014;57:530–3.CrossRefGoogle Scholar
  5. 5.
    Dearani JA, Mora BN, Nelson TJ, et al. Ebstein anomaly review: what’s now, what’s next? Expert Rev Cardiovasc Ther. 2015;13:1101–9.CrossRefGoogle Scholar
  6. 6.
    Hetzer R, Hacke P, Javier M, et al. The long-term impact of various techniques for tricuspid repair in Ebstein’s anomaly. J Thorac Cardiovasc Surg. 2015;150:1212–9.CrossRefGoogle Scholar
  7. 7.
    Ibrahim M, Tsang VT, Caruana M, et al. Cone reconstruction for Ebstein’s anomaly: patient outcomes, biventricular function, and cardiopulmonary exercise capacity. J Thorac Cardiovasc Surg. 2015;149:1144–50.CrossRefGoogle Scholar
  8. 8.
    Kapusta L, Eveleigh RM, Poulino SE, et al. Ebstein’s anomaly: factors associated with death in childhood and adolescence: a multi-centre, long-term study. Eur Heart J. 2007;28:2661–6.CrossRefGoogle Scholar
  9. 9.
    Luxford JC, Arora N, Ayer JG, et al. Neonatal Ebstein anomaly: a 30-year institutional review. Semin Thorac Cardiovasc Surg. 2017;29:206–12.CrossRefGoogle Scholar
  10. 10.
    Wald RM, Adatia I, Van Arsdell GS, Hornberger LK. Relation of limiting ductal patency to survival in neonatal Ebstein’s anomaly. Am J Cardiol. 2005;96:851–6.CrossRefGoogle Scholar
  11. 11.
    Yoo SJ, Choi YH. Ebstein’s anomaly of the tricuspid valve. In: Yoo SJ, Choi YH, editors. Angiocardiograms in congenital heart disease: teaching file of Sejong Heart Institute. Oxford/New York/Tokyo: Oxford Medical Publications; 1991. p. 84–90.Google Scholar

Copyright information

© Springer Nature Singapore Pte Ltd. 2019

Authors and Affiliations

  • In Sook Park
    • 1
  • Soo-Jin Kim
    • 2
  • Hyun Woo Goo
    • 3
  1. 1.Department of Pediatric CardiologyUniversity of Ulsan College of Medicine, Asan Medical CenterSeoulSouth Korea
  2. 2.Department of PediatricsKonkuk University Medical CenterSeoulSouth Korea
  3. 3.Department of RadiologyUniversity of Ulsan College of Medicine, Asan Medical CenterSeoulSouth Korea

Personalised recommendations