This chapter includes types, morphology, clinical manifestations, diagnosis, natural and unnatural course, treatment, and fetal diagnosis of pulmonary atresia with intact ventricular septum, including one-and-half ventricle repair and Fontan operation.
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Dyamenahalli U, McCrindle BW, McDonald C, et al. Pulmonary atresia with intact ventricular septum: management of, and outcomes for, a cohort of 210 consecutive patients. Cardiol Young. 2004;14:299–308.CrossRefGoogle Scholar
Guleserian KJ, Armsby LB, Thiagarajan RR, et al. Natural history of pulmonary atresia with intact ventricular septum and right-ventricle-dependent coronary circulation managed by the single-ventricle approach. Ann Thorac Surg. 2006;81:2250–8.CrossRefGoogle Scholar
Justo RN, Nykanen DG, Williams WG, et al. Transcatheter perforation of the right ventricular outflow tract as initial therapy for pulmonary valve atresia and intact ventricular septum in the newborn. Catheter Cardiovasc Diagn. 1997;40:408–13.CrossRefGoogle Scholar
Powell AJ, Mayer JE, Lang P, Lock JE. Outcome in infants with pulmonary atresia, intact ventricular septum, and right ventricle dependent coronary circulation. Am J Cardiol. 2000;86:1272–4.CrossRefGoogle Scholar
Reddy VM, McElhinney DB, Silverman NH, et al. Partial biventricular repair for complex congenital heart defect: an intermediate option for complicated anatomy or functionally borderline right complex heart. J Thorac Cardiovasc Surg. 1998;116:21–7.CrossRefGoogle Scholar
Schneider AW, Blom NA, Bruggemans EF, et al. More than 25 years of experience in managing pulmonary atresia with intact ventricular septum. Ann Thorac Surg. 2014;98:1680–6.CrossRefGoogle Scholar