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Vascular Disorders in the Liver

  • Masahiko Koda
  • Tomomitsu Matono
  • Makiko Taniai
  • Masaki Iwai
Chapter

Abstract

The components of the hepatic vascular system (hepatic arteries, portal and hepatic veins, sinusoids, and lymphatics) can be damaged by various injuries. Although vascular diseases in the liver are rare conditions, parts of these disorders lead to portal hypertension, hepatic failure, cirrhosis, and hepatocellular carcinoma. The progress of imaging modalities can make the diagnosis for hepatic vascular disorders easier. Imaging plays a crucial role in the early detection and assessment of the extent of hepatic vascular disorders. This article concisely reviews the classification, etiology, pathophysiology, and clinical presentation of hepatic vascular disorders and provides a detailed description of imaging and treatment options, particularly interventional management.

Keywords

Budd-Chiari syndrome Hepatic vein thrombosis Idiopathic membranous obstruction of inferior vena cava Fontan-associated liver disease Sinusoidal obstruction syndrome Veno-occlusive disease Arterioportal fistulas Idiopathic non-cirrhotic portal hypertension Portal vein thrombosis Extrahepatic portal venous obstruction Pylephlebitis Portal vein aneurysm Hereditary hemorrhagic telangiectasia Osler-Weber-Rendu disease Peliosis hepatis Portal cavernoma Hepatocellular carcinoma Portal hypertension 

Abbreviations

APF

Arterioportal fistula

AVM

Arteriovenous malformations

BCS

Budd-Chiari syndrome

CDUS

Color Doppler ultrasonography

CV

Central vein

EHPVO

Extrahepatic portal venous obstruction

FALD

Fontan-associated liver disease

FNH

Focal nodular hyperplasia

HA

Hepatic artery

HCC

Hepatocellular carcinoma

HHT

Hereditary hemorrhagic telangiectasia

HSCT

Hematopoietic stem cell transplantation

HV

Hepatic vein

INCPH

Idiopathic non-cirrhotic portal hypertension

IVC

Inferior vena cava

MOVC

Idiopathic membranous obstruction of IVC

PV

Portal vein

PVT

Portal vein thrombosis

RA

Right atrium

SMAV fistula

Superior mesenteric arteriovenous fistula

SMV

Superior mesenteric vein

SV

Splenic vein

TIPS

Transjugular intrahepatic portosystemic shunt

Notes

Acknowledgment

We are grateful to Professor Michael A. Kern for constructive advice and helpful suggestions in first edition of this chapter.

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Copyright information

© Springer Nature Singapore Pte Ltd. 2019

Authors and Affiliations

  • Masahiko Koda
    • 1
  • Tomomitsu Matono
    • 2
  • Makiko Taniai
    • 3
  • Masaki Iwai
    • 4
  1. 1.TottoriJapan
  2. 2.TottoriJapan
  3. 3.TokyoJapan
  4. 4.KyotoJapan

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