Vascular Disorders in the Liver

  • Masahiko Koda
  • Tomomitsu Matono
  • Makiko Taniai
  • Masaki Iwai


The components of the hepatic vascular system (hepatic arteries, portal and hepatic veins, sinusoids, and lymphatics) can be damaged by various injuries. Although vascular diseases in the liver are rare conditions, parts of these disorders lead to portal hypertension, hepatic failure, cirrhosis, and hepatocellular carcinoma. The progress of imaging modalities can make the diagnosis for hepatic vascular disorders easier. Imaging plays a crucial role in the early detection and assessment of the extent of hepatic vascular disorders. This article concisely reviews the classification, etiology, pathophysiology, and clinical presentation of hepatic vascular disorders and provides a detailed description of imaging and treatment options, particularly interventional management.


Budd-Chiari syndrome Hepatic vein thrombosis Idiopathic membranous obstruction of inferior vena cava Fontan-associated liver disease Sinusoidal obstruction syndrome Veno-occlusive disease Arterioportal fistulas Idiopathic non-cirrhotic portal hypertension Portal vein thrombosis Extrahepatic portal venous obstruction Pylephlebitis Portal vein aneurysm Hereditary hemorrhagic telangiectasia Osler-Weber-Rendu disease Peliosis hepatis Portal cavernoma Hepatocellular carcinoma Portal hypertension 



Arterioportal fistula


Arteriovenous malformations


Budd-Chiari syndrome


Color Doppler ultrasonography


Central vein


Extrahepatic portal venous obstruction


Fontan-associated liver disease


Focal nodular hyperplasia


Hepatic artery


Hepatocellular carcinoma


Hereditary hemorrhagic telangiectasia


Hematopoietic stem cell transplantation


Hepatic vein


Idiopathic non-cirrhotic portal hypertension


Inferior vena cava


Idiopathic membranous obstruction of IVC


Portal vein


Portal vein thrombosis


Right atrium

SMAV fistula

Superior mesenteric arteriovenous fistula


Superior mesenteric vein


Splenic vein


Transjugular intrahepatic portosystemic shunt



We are grateful to Professor Michael A. Kern for constructive advice and helpful suggestions in first edition of this chapter.


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Copyright information

© Springer Nature Singapore Pte Ltd. 2019

Authors and Affiliations

  • Masahiko Koda
    • 1
  • Tomomitsu Matono
    • 2
  • Makiko Taniai
    • 3
  • Masaki Iwai
    • 4
  1. 1.TottoriJapan
  2. 2.TottoriJapan
  3. 3.TokyoJapan
  4. 4.KyotoJapan

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