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Megacystis Microcolon Intestinal Hypoperistalsis Syndrome: MMIHS

  • Hideki SohEmail author
Chapter

Abstract

Megacystis microcolon intestinal hypoperistalsis syndrome (MMIHS) is a rare congenital condition, and such patients tend to present with abdominal distension, a largely dilated nonobstructive bladder, microcolon, and severe functional intestinal obstruction without structural atresia or stenosis in the neonatal period. Currently, the etiology is not well understood, and there is no specific treatment for this condition. The majority of MMIHS patients repeat the intestinal obstruction and enteritis, so they require long-term PN and drainage stomas. The prognosis remains poor.

Keywords

Megacystis microcolon intestinal hypoperistalsis syndrome (MMIHS) Functional intestinal obstruction Nonobstructed urinary bladder distention 

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Copyright information

© Springer Nature Singapore Pte Ltd. 2019

Authors and Affiliations

  1. 1.Department of Pediatric SurgeryOsaka Women’s and Children’s HospitalIzumiJapan

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