Intraocular Medulloepithelioma

  • Shweta Rathi Gupta
  • Swathi Kaliki
Part of the Retina Atlas book series (RA)


Intraocular medulloepithelioma is a rare embryonal neuroepithelial tumor that originates from the undifferentiated medullary epithelium over the ciliary body or inner layer of the optic cup (Zimmerman 1971; Fuchs 1908). It commonly arises from the nonpigmented ciliary epithelium of the pars plicata and rarely in the iris, retina, optic nerve, and the central nervous system (Verhoeff 1904; Takei et al. 2007; Morris and Garner 1975; Vadmal et al. 1996; Green et al. 1974; Chavez et al. 2004; Sundaram et al. 2003; Steinkuller and Font 1997).


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Copyright information

© Springer Nature Singapore Pte Ltd. 2019

Authors and Affiliations

  • Shweta Rathi Gupta
    • 1
  • Swathi Kaliki
    • 1
  1. 1.Ocular Oncology ServiceThe Operation Eyesight Universal Institute for Eye Cancer (SRG, SK), L V Prasad Eye InstituteHyderabadIndia

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