Congenital Abnormalities of the Fundus and Retinal Detachment

  • Yao Huang
  • Nan Zhou
  • Wenbin Wei


This chapter deals with congenital abnormalities of the fundus and retinal detachment. Congenital abnormalities of the fundus include morning glory syndrome, a specific congenital papillary dysplasia. Congenital optic disc pit is a type of congenital optic disc abnormality. Congenital coloboma of the optic disc can occur secondary to serous retinal detachment in the macular area or elsewhere. Large areas of myelinated nerve fibers can be manifested as “white pupils” and have been misdiagnosed as retinal detachment. Sometimes retinal detachment can occur in a choroid coloboma, and the hole is often located at the edge of the sclera. The main feature of Coats Disease, also known as external exudative retinopathy, is idiopathic retinal telangiectasia. Retinoschisis is the separation of layers within the retinal neuroepithelium, and it should be differentiated from rhegmatogenous retinal detachment.


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Copyright information

© Springer Nature Singapore Pte Ltd. and Beijing Science and Technology Press 2018

Authors and Affiliations

  • Yao Huang
    • 1
  • Nan Zhou
    • 1
  • Wenbin Wei
    • 1
  1. 1.Beijing Tongren Eye Center, Beijing Tongren Hospital, Capital Medical UniversityBeijingChina

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