IgG4-Related Sclerosing Cholangitis in Europe
IgG4-related sclerosing cholangitis (IgG4-RC) is a clinical condition described in the last 10 years, according to the growing knowledge on IgG4-related diseases (IgG4-RD). In Europe, few studies have been published on IgG4-RC and the information available are mainly derived from patients suffering from autoimmune pancreatitis (AIP). The chapter report the knowledge about the disease in Europe, and diagnostic algorytm and therapy currently applied for this rare but challenging disease.
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