• Atsushi TanakaEmail author


Immunoglobulin G4-related sclerosing cholangitis (IgG4-SC) is a relatively new disease entity, thus very limited data are currently available regarding its epidemiology. To date, several case series regarding clinical profiles of IgG4-SC have been published, including our study [1–3]; however, no epidemiological studies illustrating the incidence and prevalence of IgG4-SC have been conducted. In this review, epidemiological and clinical features of IgG4-SC are discussed in general and are based mainly on data in the Japanese population.


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Copyright information

© Springer Science+Business Media Singapore 2019

Authors and Affiliations

  1. 1.Department of MedicineTeikyo University School of MedicineTokyoJapan

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