Experimental protoporphyria in hairless mice: Photodermatitis

  • H. Baart De La Faille
  • R. A. Woutersen
  • H. Van Weelden
  • E. H. Baart De La Faille-Kuyper
Part of the Inflammation: Mechanisms and Treatment book series (FTIN, volume 4)


Erythropoietic protoporphyria (EPP) is an inheritable inborn error of human metabolism giving rise to an excess production and accumulation of the haem precursor protoporphyrin1–3. Increased concentrations of protoporphyrin can be demonstrated in, for example, erythrocytes, and to a smaller extent also in plasma. The excretion of the substance in faecal matter is often elevated; urinary porphyrins are always normal.


Skin Thickness Hairless Mouse Violet Light Urinary Porphyrin Erythropoietic Protoporphyria 
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Copyright information

© MTP Press Limited 1980

Authors and Affiliations

  • H. Baart De La Faille
    • 1
  • R. A. Woutersen
    • 1
  • H. Van Weelden
    • 1
  • E. H. Baart De La Faille-Kuyper
    • 1
  1. 1.Netherlands

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