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Primäre Krankheiten des Lungenparenchyms

  • P. Birrer
  • H. Lindemann
  • G. Kusenbach
  • N. Teig
  • H. von der Hardt
Chapter
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Zusammenfassung

Die interstitiellen Pneumopathien sind eine ätiologisch heterogene Gruppe von Lungenkrankheiten (Übersicht 12.1), die sich klinisch, radiologisch und lungenphysiologisch ähnlich manifestieren. Im Verlauf können sie sich sehr unterschiedlich präsentieren, ihr gemeinsames Ende finden sie in einer mehr oder weniger ausgeprägten Lungenfibrose, die sich aber in ihrem Endstadium — sei das nach (Defekt-)Heilung oder terminal in der schweren Lungenfibrose — nicht mehr ätiopathogenetisch differenzieren läßt. Während die Diagnose einer interstitiellen Pneumopathie recht einfach gestellt werden kann, verlangt die ätiologische Zuordnung die Interpretation der Anamnese, der klinischen Manifestation und von vielen Einzeluntersuchungen und setzt hohes fachliches Wissen und Erfahrung voraus. Die meisten interstitiellen Pneumopathien sind selten, insbesondere im Kindesalter. Untersuchungstechniken und Behandlungsstrategien werden deshalb von den Erwachsenen übernommen.

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Copyright information

© Springer-Verlag Berlin Heidelberg 1999

Authors and Affiliations

  • P. Birrer
  • H. Lindemann
  • G. Kusenbach
  • N. Teig
  • H. von der Hardt

There are no affiliations available

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