Pain pp 1265-1268 | Cite as


  • Ashish GulveEmail author


Erythromelalgia is a rare disorder of the extremities in which there is burning pain that is frequently aggravated by heat or by lowering the extremity. This is the first human disorder in which an ion channel mutation (Na(v) 1.7) is associated with chronic neuropathic pain. This chapter discusses the fundamental pathogenesis, types of Erythromelalgia, clinical findings, and treatment modalities for Erythromelalgia.


Erythromelalgia Neuropathic pain Neuropathy Vasculopathy 


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Copyright information

© Springer Nature Switzerland AG 2019

Authors and Affiliations

  1. 1.Department of Pain ManagementThe James Cook University HospitalMiddlesbroughUK

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