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Treatment of Oromandibular Dystonia

  • Stewart A. FactorEmail author
  • Laura M. Scorr
Chapter
  • 496 Downloads
Part of the Current Clinical Neurology book series (CCNEU)

Abstract

Oromandibular dystonia (OMD) is a rare form of dystonia that affects the masticatory, lower facial, and lingual muscles. OMD is often idiopathic and can present as a focal dystonia or as part of a segmental or generalized pattern of dystonia. The movement phenotypes of OMD include jaw opening, jaw closing, lateral jaw deviation, lingual protrusion, and mixed presentations. Diagnosis and treatment initiation are often delayed because OMD is under-recognized. Meanwhile these patients endure significant disability, because eating and speaking are impaired, which has a negative impact on quality of life. Botulinum toxin injections are the most effective therapeutic strategy. The technique and onabotulinumA toxin doses for jaw injection are described.

Keywords

Oromandibular dystonia Lingual dystonia Botulinum toxin 

Supplementary material

Video 1

This video shows the patient Oromandibular dystonia (OMD) patient history at baseline with jaw-opening and lingual protrusion dystonia. I also demonstrate difficulty speaking and eating and impact of her trick (MPG 16115 kb)

Suggested Reading

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Copyright information

© Springer Nature Switzerland AG 2019

Authors and Affiliations

  1. 1.Vance Lanier Chair of Neurology, Department of NeurologyJean and Paul Amos Parkinson’s Disease and Movement Disorder Program, Emory UniversityAtlantaUSA
  2. 2.Department of NeurologyJean and Paul Amos Parkinson’s Disease and Movement Disorder Program, Emory University School of MedicineAtlantaUSA

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