Congenital Anomalies of the Kidney and Urinary Tract in Adolescents

  • Erica WinnickiEmail author
  • Hillary Copp


Congenital anomalies of the kidney and urinary tract are a heterogeneous group of disorders which represent the most common cause of chronic kidney disease in children and adolescents. Children are most often diagnosed in the antenatal and neonatal period given the widespread use of antenatal ultrasound; however, late diagnoses do occur and clinicians should recognize potential presenting signs and symptoms. Care of children with chronic kidney disease due to congenital anomalies of the kidney and urinary tract should be undertaken by a multidisciplinary team that includes both a pediatric urologist and pediatric nephrologist. Treatment involves surgical interventions and management of bladder dysfunction in some cases, as well as medical management of the complications of chronic kidney disease. Particular attention should be paid to the adolescent with chronic kidney disease due to congenital anomalies of the kidney and urinary tract as puberty is a time of more rapid kidney disease progression. For those children who do progress to end-stage renal disease, outcomes with renal transplantation are superior in this group of patients as compared to other causes of renal disease.


CAKUT PUV Chronic kidney disease 


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Copyright information

© Springer Nature Switzerland AG 2019

Authors and Affiliations

  1. 1.Department of Pediatrics, Division of NephrologyUniversity of California San FranciscoSan FranciscoUSA
  2. 2.Department of UrologyUniversity of California San FranciscoSan FranciscoUSA

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