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Juvenile Dermatomyositis in Adolescents and Young Adults

  • Christina Ann BorosEmail author
Chapter
Part of the In Clinical Practice book series (ICP)

Abstract

Juvenile dermatomyositis (JDM) is a rare disease but the most common idiopathic inflammatory myopathy (IIM) of childhood. It is a systemic vasculopathy primarily affecting the skin and muscles, causing classic signs of rash and proximal muscle weakness, but can present with heterogeneous features, natural history and outcomes. This chapter highlights the differences between paediatric and adult disease in clinical presentation and presents an update of treatment strategies and outcomes of the disease including cardiovascular involvement, reproductive health and vocational developmental milestones.

Keywords

Juvenile dermatomyositis Cardiovascular involvement Long-term outcomes Calcinosis 

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Copyright information

© Springer Nature Switzerland AG 2019

Authors and Affiliations

  1. 1.Women’s and Children’s HospitalAdelaideAustralia
  2. 2.University of AdelaideAdelaideAustralia

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