Autoinflammatory Conditions in Adolescence and Young Adulthood

  • Eileen BaildamEmail author
Part of the In Clinical Practice book series (ICP)


Autoinflammatory conditions (AIC) or hereditary recurrent fevers (HRF) include recently identified, very rare conditions usually presenting in childhood with a wide range of severities. This chapter summarizes current knowledge of AIC and their management during adolescence and young adulthood. Some AIC are well characterized, but new features and syndromes are being identified making this an evolving field. AIC require multidisciplinary care combining pediatric/adolescent/adult rheumatology, immunology, and infectious disease professionals, all with a focused special interest in the field and linked with national specialist services.


Autoinflammatory conditions Hereditary recurrent fevers Amyloidosis 


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© Springer Nature Switzerland AG 2019

Authors and Affiliations

  1. 1.Alder Hey Children’s Foundation NHS TrustLiverpoolUK

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