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Pulmonary Hypertension

  • Peter M. Hickey
  • Robin Condliffe
  • Allan Lawrie
  • David G. Kiely
Chapter

Abstract

While pulmonary hypertension is readily diagnosed at cardiac catheterisation, delayed recognition and targeting treatment to the underlying cause can be challenging. Modern classification distinguishes between pulmonary hypertension secondary to cardiac disease, hypoxia with or without lung disease, thromboembolic pulmonary vascular disease, pulmonary hypertension associated with systemic diseases, and idiopathic forms. The physiological consequences and the use of various imaging modalities in refining diagnosis are discussed. For patients with idiopathic pulmonary hypertension, novel pharmacological approaches, either singly or in combination, have been more rigorously evaluated, and the use of surgery for chronic thromboembolic pulmonary hypertension is now well established.

Keywords

Definition and classification Diagnostic strategies Investigation Imaging Cardiac catheterisation Pregnancy Anaesthesia Sepsis Pulmonary arterial hypertension Left heart disease Chronic lung disease Chronic thromboembolic disease Pulmonary endarterectomy Targeted treatments 

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Copyright information

© Springer International Publishing AG, part of Springer Nature 2018

Authors and Affiliations

  • Peter M. Hickey
    • 1
  • Robin Condliffe
    • 2
  • Allan Lawrie
    • 3
  • David G. Kiely
    • 2
  1. 1.Pulmonary Vascular Research Group, Department of Infection, Immunity and Cardiovascular Disease (IICD)University of SheffieldSheffieldUK
  2. 2.Pulmonary Vascular Disease UnitRoyal Hallamshire Hospital, Sheffield Teaching Hospitals NHS TrustSheffieldUK
  3. 3.Pulmonary Vascular Research Group, Department of Infection, Immunity and Cardiovascular DiseaseUniversity of SheffieldSheffieldUK

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