Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome is a rare congenital abnormality of the female genital tract. It is characterized by aplasia of the uterus and the upper two-thirds of the vagina.
The syndrome is caused by embryologic growth failure of the Mullerian ducts, with an incidence of almost one in 4000 female newborns.
Clinical examination, pelvic, and renal ultrasound as well as laparoscopy confirm the diagnosis of the syndrome.
Following the Creatsas vaginoplasty, a functioning vagina of 10–12 cm in depth and 5 cm in width is created in 95.5% of the cases. In addition, almost all cases declared themselves to have a satisfactory quality of sexual life, while less than 5% of the cases report an adequate one. Creatsas vaginoplasty is a simple, quick, and effective vulvo-perineoplasty for reconstruction of vaginal aplasia.
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