Incidence of Moyamoya Disease in Denmark: A Population-Based Register Study

  • Peter Birkeland
  • Jens Lauritsen
Conference paper
Part of the Acta Neurochirurgica Supplement book series (NEUROCHIRURGICA, volume 129)


In this first population-based study of moyamoya disease (MMD) in Europe, the authors identified 56 patients with MMD in Denmark during the period 1994–2015 using nationwide registers. The overall incidence was 0.047 per 100,000 person-years, which is about one-tenth that reported in Japan. Otherwise the epidemiological features were comparable: there was a bimodal age distribution with peaks in the age groups 0–9 years and 30–39 years, with twice as many females as males.


Moyamoya disease Epidemiology Stroke Cerebrovascular 1994–2015 Scandinavian 


Ethics and Conflict of Interest

Ethical Approval

For this type of study formal consent is not required.

Conflict of Interest

The authors declare that they have no conflict of interest.


This study was supported by a grant from Ingeniør K.A. Rohde of Hustrus Legat.


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Copyright information

© Springer International Publishing AG, part of Springer Nature 2018

Authors and Affiliations

  1. 1.Department of NeurosurgeryAalborg University HospitalAalborgDenmark
  2. 2.Department of Orthopaedic SurgeryOdense University HospitalOdenseDenmark
  3. 3.Institute of Clinical ResearchUniversity of Southern DenmarkOdenseDenmark

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