Erythema Elevatum Diutinum

  • Anh N. Tran
  • Joseph L. Jorizzo


Erythema elevatum diutinum can be thought of as a rare presentation of chronic cutaneous vasculitis. Although the exact pathogenesis is unknown, it has been associated with a wide range of clinical illnesses including IgA monoclonal gammopathy, myelodysplastic syndrome, rheumatoid arthritis, inflammatory bowel disease, streptococcal infection, and HIV. Lesions typically present as asymptomatic, red-brown papules and nodules symmetrically distributed with a predilection for skin overlying joints, buttocks, and the Achilles tendon. Dapsone is considered first-line treatment.



We thank Omar Sangueza, MD, Professor of Pathology and Dermatology, Wake Forest University School of Medicine for photographs and histology.


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Copyright information

© Springer International Publishing AG, part of Springer Nature 2018

Authors and Affiliations

  • Anh N. Tran
    • 1
  • Joseph L. Jorizzo
    • 1
  1. 1.Department of DermatologyWeill Cornell MedicineNew YorkUSA

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