Vitiligo pp 41-51 | Cite as

Vitiligo/nonsegmental Vitiligo Including Acrofacial and Universalis

  • Thierry Passeron
  • Jean-Paul Ortonne
  • Prasad Kumarasinghe
  • Alain TaïebEmail author


Based on the VGICC classification, vitiligo/NSV, a consensus umbrella term for all forms of generalized vitiligo, is meant to describe different clinical subtypes of vitiligo that are all clearly distinct from SV including acrofacial, generalized, mucosal (multifocal), and universal. According to the VETF definition, generalized vitiligo is characterized by asymptomatic well-circumscribed milky-white macules involving both sides of the body with usually a symmetrical pattern. In acrofacial vitiligo (AFV), the involved sites are by definition limited to the face, head, hands, and feet with typically depigmentation of the distal fingers and facial orifices. Vitiligo universalisis a rapidly progressive form of the disease, which needs a more in-depth investigation especially for associated autoimmunity.



Dr. Prasad Kumarasinghe is grateful to Prof. Roy Chan, Medical Director, and Dr. Goh Boon Kee, Consultant Dermatologist, National Skin Centre, Singapore, for providing some of the VU photographs.


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Copyright information

© Springer Nature Switzerland AG 2019

Authors and Affiliations

  • Thierry Passeron
    • 1
  • Jean-Paul Ortonne
    • 2
  • Prasad Kumarasinghe
    • 3
  • Alain Taïeb
    • 4
    Email author
  1. 1.Department of DermatologyUniversity Hospital of NiceNiceFrance
  2. 2.Department of DermatologyArchet-2 hospitalNiceFrance
  3. 3.Department of DermatologyRoyal Perth HospitalPerthAustralia
  4. 4.Service de DermatologieHôpital St André, CHU de BordeauxBordeauxFrance

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