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Hemophilia A and B

  • James P. R. BrownEmail author
  • Joanne Douglas
Chapter

Abstract

This chapter outlines the pathophysiology, clinical presentation, inheritance, and incidence of hemophilia A and B. The chapter describes the interaction with pregnancy and discusses the medical and anesthetic management of pregnant women with hemophilia A and B, including treatment of acute hemorrhage.

Keywords

Hemophilia A Hemophilia B Factor VIII deficiency Factor IX deficiency Christmas disease Inherited bleeding disorder Inherited coagulopathy 

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Copyright information

© Springer International Publishing AG, part of Springer Nature 2018

Authors and Affiliations

  1. 1.UBC Department of Anesthesiology, Pharmacology and TherapeuticsBC Women’s HospitalVancouverCanada
  2. 2.Department of AnesthesiaBC Women’s HospitalVancouverCanada

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