This chapter outlines the pathophysiology, clinical presentation, inheritance, and incidence of fibrinogen deficiency. The chapter describes the interaction with pregnancy and discusses the medical and anesthetic management of pregnant women with fibrinogen deficiency, including treatment of acute hemorrhage.
KeywordsFibrinogen deficiency Factor I deficiency Afibrinogenemia Hypofibrinogenemia Dysfibrinogenemia Inherited bleeding disorder Inherited coagulopathy
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