Pineal Region Tumors

  • Nicholas TrakulEmail author
  • Jason Ye


This chapter describes the four recognized histologic types of pineal parenchymal tumors (PPTs). Clinical presentation and common signs and symptoms caused by tumors of the pineal region are described. Clinical workup, including relevant imaging studies and laboratory testing, is outlined. The general treatment approach is considered. Roles of surgery, chemotherapy, and radiation in the definitive and adjuvant setting are discussed for each histologic type. Radiation therapy techniques are described in detail. Included are delineation of treatment volumes, commonly used treatment doses, and treatment delivery systems, including stereotactic radiosurgery and intensity-modulated radiotherapy (IMRT). Possible acute and chronic radiation toxicities and suggestions for posttreatment surveillance conclude the chapter.


Pineal parenchymal tumor Pineocytoma Pineal parenchymal tumors of intermediate differentiation Pineoblastoma Papillary tumors of the pineal region Stereotactic radiosurgery 


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Copyright information

© Springer International Publishing AG, part of Springer Nature 2018

Authors and Affiliations

  1. 1.Department of Radiation OncologyStanford UniversityStanfordUSA
  2. 2.Department of Radiation OncologyKeck School of Medicine of USCLos AngelesUSA

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