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Basic Echocardiography in Arrhythmogenic Right Ventricular Cardiomyopathy

  • Andreea M. DragosEmail author
  • Bruno Pinamonti
  • Elena Abate
Chapter

Abstract

Two-dimensional echocardiography represents a fundamental imaging tool in the diagnosis and follow-up of patients with arrhythmogenic right ventricular cardiomyopathy (ARVC); quantitative assessment of RV dimensions and function represents a key element by which to achieve formal diagnosis in this pathology. Evaluation of RV morphology and function using 2D echocardiography is difficult due to the complex geometry of the RV chamber and to the lack of standardization of RV measurements in common clinical practice. Nevertheless, a complete qualitative and quantitative assessment of the RV is crucial in ARVC due to the typical morphofunctional features of the disease. Furthermore, left ventricular involvement and tricuspid regurgitation are frequent in ARVC patients and represent important parameters for prognostic stratification.

Keywords

Right Ventricular Right Ventricular Outflow Tract Arrhythmogenic Right Ventricular Cardiomyopathy Right Ventricular Systolic Function Right Ventricular Wall 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

Supplementary material

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References

  1. 1.
    Sen-Chowdhry S, Syrris S, Prasad SK et al (2008) Left-dominant arrhythmogenic cardiomyopathy: an under-recognized clinical entity. J Am Coll Cardiol 52:2175–2187PubMedCrossRefGoogle Scholar
  2. 2.
    Marcus FI, McKenna WJ, Sherrill D et al (2010) Diagnosis of arrhythmogenic right ventricular cardiomyopathy/dysplasia: proposed modification of the Task Force Criteria. Eur Heart J 31:806–814PubMedCrossRefPubMedCentralGoogle Scholar
  3. 3.
    Yoerger DM, Marcus F, Sherrill D et al (2005) Echocardiographic findings in patients meeting task force criteria for arrhythmogenic right ventricular dysplasia: new insights from the multidisciplinary study of right ventricular dysplasia. J Am Coll Cardiol 45:860–865PubMedCrossRefGoogle Scholar
  4. 4.
    Rudski LG, Lai WW, Afilalo L et al (2010) Guidelines for the echocardiographic assessment of the right heart in adults: a report from the American Society of Echocardiography endorsed by the European Association of Echocardiography, a registered branch of the European Society of Cardiology, and the Canadian Society of Echocardiography. J Am Soc Echocardiogr 23:685–713; quiz 786–788PubMedCrossRefGoogle Scholar
  5. 5.
    Anavekar NS, Gerson D, Skali H et al (2007) Two-dimensional assessment of right ventricular function: an echocardiographic-MRI correlative study. Echocardiography 24:452–456PubMedCrossRefGoogle Scholar
  6. 6.
    Anavekar NS, Skali H, Bourgoun M et al (2008) Usefulness of right ventricular fractional area change to predict death, heart failure, and stroke following myocardial infarction (from the VALIANT ECHO Study). Am J Cardiol 101:607–612PubMedCrossRefGoogle Scholar
  7. 7.
    Hulot JS, Jouven X, Emoana JP et al (2004) Natural history and risk stratification of arrhythmogenic right ventricular dysplasia/cardiomyopathy. Circulation 110:1879–1884PubMedCrossRefGoogle Scholar
  8. 8.
    Pinamonti B, Dragos AM, Pyxaras SA et al (2011) Prognostic predictors in arrhythmogenic right ventricular cardiomyopathy: results from a 10-year registry. Eur Heart J 32:1105–1113PubMedCrossRefGoogle Scholar
  9. 9.
    McKenna WJ, Thiene G, Nava A et al (1994) Diagnosis of arrhythmogenic right ventricular dysplasia/cardiomyopathy. Task Force of the Working Group Myocardial and Pericardial Disease of the European Society of Cardiology and of the Scientific Council on Cardiomyopathies of the International Society and Federation of Cardiology. Br Heart J 71:215–218PubMedCrossRefPubMedCentralGoogle Scholar
  10. 10.
    Marcus FI, Fontaine GH, Guiraudon G et al (1982) Right ventricular dysplasia: a report of 24 adult cases. Circulation 65:384–398PubMedCrossRefGoogle Scholar
  11. 11.
    Scognamiglio R, Fasoli G, Nava A et al (1989) Contribution of cross-sectional echocardiography to the diagnosis of right ventricular dysplasia at the asymptomatic stage. Eur Heart J 10:538–542PubMedCrossRefGoogle Scholar
  12. 12.
    Sievers B, Marvin A, Ulrich F et al (2004) Right ventricular wall motion abnormalities found in healthy subjects by cardiovascular magnetic resonance imaging and characterized with a new segmental model. J Cardiovasc Magn Reson 6:601–608PubMedCrossRefGoogle Scholar
  13. 13.
    Van den Bosch AE, Meijiboom FJ, McGhie JS et al (2004) Enhanced visualization of the right ventricle by contrast echocardiography in congenital heart disease. Eur J Echocardiogr 5:104–110PubMedCrossRefGoogle Scholar
  14. 14.
    Pinamonti B, Sinagra G, Salvi A et al (1992) Left ventricular involvement in right ventricular dysplasia. Am Heart J 123:711–724PubMedCrossRefGoogle Scholar
  15. 15.
    Corrado D, Basso C, Thiene G et al (1997) Spectrum of clinicopathologic manifestations of arrhythmogenic right ventricular cardiomyopathy/dysplasia: a multicenter study. J Am Coll Cardiol 30:1512–1520PubMedCrossRefGoogle Scholar
  16. 16.
    Pinamonti B, Pagnan L, Bussani R et al (1998) Images in cardiovascular medicine: right ventricular dysplasia with biventricular involvement. Circulation 98:1943–1945PubMedCrossRefGoogle Scholar
  17. 17.
    Pinamonti B, Di Lenarda A, Sinagra G et al (1995) Long-term evolution of right ventricular dysplasia-cardiomyopathy. Am Heart J 129:412–415Google Scholar

Copyright information

© Springer International Publishing Switzerland 2014

Authors and Affiliations

  • Andreea M. Dragos
    • 1
    Email author
  • Bruno Pinamonti
    • 1
  • Elena Abate
    • 1
  1. 1.Department of CardiologyUniversity Hospital of TriesteTriesteItaly

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