Unilateral Congenital Cataracts

  • Crystal S. Y. Cheung
  • Bharti R. NihalaniEmail author


Unilateral congenital cataracts are believed to result from localized ocular dysgenesis. Approximately 80–90% of unilateral cataracts are idiopathic. They are rarely associated with systemic anomalies and hence do not require systemic workup. Nuclear cataracts are common. Posterior capsule plaques are frequently encountered with unilateral congenital cataracts. Persistent fetal vasculature (PFV) poses special challenges in management. Early diagnosis and prompt treatment are critical for visually significant unilateral congenital cataracts owing to competition from the dominant normal eye. Preoperative counselling should stress the importance of full-time optical correction and amblyopia management. The visual outcomes are limited by early onset of deprivation amblyopia.


Unilateral congenital cataract Preoperative evaluation of congenital cataract Deprivation amblyopia 



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Copyright information

© Springer Nature Switzerland AG 2020

Authors and Affiliations

  1. 1.Boston Children’s Hospital, Harvard Medical SchoolBostonUSA

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