Phenomenology of Ataxia

  • Steven J. FruchtEmail author
  • Pichet Termsarasab


Evaluation of patients with ataxia aims to identify patients with reversible or treatable etiologies and to secure diagnoses and improve quality of life in other patients. The movement disorder history offers important clues to the diagnosis.


Ataxia Dysmetria Tremor Opsoclonus Ocular flutter 

Supplementary material

Video 10.1

This chapter videos cover a diverse group of patients and phenomenologies with the shared phenotype of ataxia. The videos are divided into five segments: autosomal recessive ataxias; autosomal dominant ataxias; structural ataxias; inflammatory ataxias; and paraneoplastic ataxias (MP4 8679089 kb)


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© Springer Nature Switzerland AG 2020

Authors and Affiliations

  1. 1.Division of Movement DisordersNew York University Grossman School of Medicine, The Marlene and Paolo Fresco Institute for Parkinson’s and Movement Disorders, NYU Langone HealthNew YorkUSA
  2. 2.Division of Neurology, Faculty of MedicineRamathibodi Hospital, Mahidol UniversityBangkokThailand

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