• Wojciech BaranEmail author
  • Jacek Szepietowski


  • Pityriasis rubra pilaris (PRP) is an idiopathic, papulosquamous disease with two age peaks in the first and fifth decade of life

  • Type III PRP, called “juvenile classical”, can result in erythroderma with islands of sparing called “nappes claires”

  • Classical juvenile PRP, as diagnosed in our patient typically resolves within 1 year

  • In severe cases, patients might require few months of systemic treatment

  • In severe cases of erythrodermic PRP supportive care is indicated to prevent hypothermia, electrolyte imbalance and protein loss


Pityriasis rubra pilaris Papulosquamous Nappes claires Acitretin 


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Copyright information

© Springer Nature Switzerland AG 2020

Authors and Affiliations

  1. 1.Department of Dermatology, Venereology and AllergologyWroclaw Medical UniversityWrocławPoland

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