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Erythroderma

  • Wojciech BaranEmail author
  • Jacek Szepietowski
Chapter

Abstract

  • Pityriasis rubra pilaris (PRP) is an idiopathic, papulosquamous disease with two age peaks in the first and fifth decade of life

  • Type III PRP, called “juvenile classical”, can result in erythroderma with islands of sparing called “nappes claires”

  • Classical juvenile PRP, as diagnosed in our patient typically resolves within 1 year

  • In severe cases, patients might require few months of systemic treatment

  • In severe cases of erythrodermic PRP supportive care is indicated to prevent hypothermia, electrolyte imbalance and protein loss

Keywords

Pityriasis rubra pilaris Papulosquamous Nappes claires Acitretin 

References

  1. 1.
    Fuchs-Telem D. Familial pityriasis rubra pilaris is caused by mutations in CARD14. Am J Hum Genet. 2012;91(1):163–70.CrossRefGoogle Scholar
  2. 2.
    Allison D. Pityriasis rubra pilaris in children. J Am Acad Dermatol. 2002;47(3):386–9.CrossRefGoogle Scholar
  3. 3.
    Eastham A. Treatment options for pityriasis rubra pilaris including biologic agents: a retrospective analysis from an academic medical center. JAMA Dermatol. 2014;150(1):92–4.CrossRefGoogle Scholar

Copyright information

© Springer Nature Switzerland AG 2020

Authors and Affiliations

  1. 1.Department of Dermatology, Venereology and AllergologyWroclaw Medical UniversityWrocławPoland

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