Persistent, Annular Urticarial Plaque

  • Selcen Kundak
  • Malik Ergin


  • Urticarial vasculitis is one type of chronic urticaria associated with vasculitic features

  • Urticarial vasculitis typically presents as erythematous wheals that resemble urticarial lesions and last more than 24 h

  • Patients with urticarial vasculitis and hypocomplementemia have a higher probability of systemic involvement

  • Hypocomplementemia is usually observed and the hypocomplementemic urticarial vasculitis (HUV) subtype, and can be associated with autoimmune connective tissue diseases including Sjögren’s syndrome and systemic lupus erythematosus (SLE)

  • HUV is identified in about 5% of patients with urticarial vasculitis and more than 50% of these patients develop SLE over time


Urticarial vasculitis Hypocomplementemia Sjögren’s syndrome Systemic lupus erythematosus 


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Copyright information

© Springer Nature Switzerland AG 2020

Authors and Affiliations

  • Selcen Kundak
    • 1
  • Malik Ergin
    • 2
  1. 1.Department of DermatologyDr. Behçet Uz Children’s HospitalİzmirTurkey
  2. 2.Department of PathologyDr. Behçet Uz Children’s HospitalİzmirTurkey

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