Complete Atrioventricular Septal Defect

  • Tom R. KarlEmail author
  • Nelson Alphonso
  • John S. K. Murala
  • Kanchana Singappulli


Complete atrioventricular septal defect (AVSD) is a complex and relatively common congenital cardiac defect. The prognosis without surgical correction is generally quite poor. Current practice in most centers is repair in infancy, usually around 3–4 months of age. Repair involves septation of the atrium and ventricles, as well as partitioning and repair of the common AV valve. The Nunn repair is our preferred technique, although other operative strategies have been applied successfully over the years. All available techniques are technically demanding. Results of surgery in thousands of cases suggest that the natural history of this disease has been improved significantly.


Complete atrioventricular septal defect Left atrioventricular valve Nunn repair Right atrioventricular valve Two patch repair 


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Copyright information

© Springer Nature Switzerland AG 2020

Authors and Affiliations

  • Tom R. Karl
    • 1
    • 2
    Email author
  • Nelson Alphonso
    • 3
  • John S. K. Murala
    • 4
  • Kanchana Singappulli
    • 5
  1. 1.Heart InstituteJohns Hopkins All Children’s HospitalSt. PetersburgUSA
  2. 2.Johns Hopkins School of MedicineSan FranciscoUSA
  3. 3.Queensland Paediatric Cardiac ServiceLady Cilento Children’s HospitalBrisbaneAustralia
  4. 4.Department of Cardiovascular and Thoracic SurgeryUniversity of Texas Southwestern Medical CenterDallasUSA
  5. 5.Department of Pediatric Cardiac SurgeryLady Ridgeway Hospital for ChildrenColomboSri Lanka

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