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Rheumatology

  • Amanda G. BrownEmail author
  • William Blaine Lapin
  • Andrea A. Ramirez
  • Jennifer L. Rammel
Chapter

Abstract

This is a brief but comprehensive overview of topics that will be tested in the pediatric board exams. It covers a wide range of pediatric rheumatology conditions, including juvenile idiopathic arthritis (JIA), juvenile systemic lupus erythematosus (jSLE), vasculitis, and others, focusing on clinical presentation, differential diagnoses, pathophysiology, workup, classic laboratory features, and treatment options. This is a high-yield review for exam preparation with pearls and pitfalls at the end of the chapter.

Keywords

Juvenile idiopathic arthritis (JIA) Enthesitis-related arthritis (ERA) Macrophage activation syndrome (MAS) Uveitis Acute rheumatic fever Juvenile systemic lupus erythematosus (jSLE) Neonatal lupus erythematosus (NLE) Drug-induced lupus (DIL) Systemic scleroderma Localized scleroderma Post-streptococcal reactive arthritis (PSRA) Mixed connective tissue disease (MCTD) Sjögren syndrome Juvenile dermatomyositis (JDM) Polymyositis Periodic fever Aphthous stomatitis Pharyngitis Cervical adenitis syndrome (PFAPA) Familial Mediterranean fever (FMF) Chronic recurrent multifocal osteomyelitis (CRMO) Amplified musculoskeletal pain syndrome (AMPS) Granulomatosis with polyangiitis (GPA) Microscopic polyangiitis (MPA) Takayasu arteritis (TA) Behçet disease Henoch-Schönlein purpura (HSP) 

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Copyright information

© Springer Nature Switzerland AG 2020

Authors and Affiliations

  • Amanda G. Brown
    • 1
    Email author
  • William Blaine Lapin
    • 1
  • Andrea A. Ramirez
    • 1
  • Jennifer L. Rammel
    • 1
  1. 1.Division of Rheumatology, Department of PediatricsBaylor College of MedicineHoustonUSA

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