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Kidney Malformation and Persistent Neutropenia

  • Mihaela Tatiana Bataneant
Chapter

Abstract

Warts, Hypogammaglobulinemia, Immunodeficiency, and Myelokathexis (WHIM) syndrome is characterized by warts, hypogammaglobulinemia, immunodeficiency, and myelokathexis. Absence of myelokathexis excludes the diagnosis

An important diagnostic features of the neutropenia of WHIM syndrome is the elevation of neutrophil count during infections and a rapid response to low doses of granulocyte colony stimulating factor (G-CSF)

Prognosis for WHIM depends in part on early recognition of the disorder, with aggressive medical intervention to reduce the frequency of recurrent bacterial infections and to detect and extirpate early HPV lesions that appear to be dysplastic or malignant

Keywords

Warts, Hypogammaglobulinemia, Immunodeficiency, and Myelokathexis Granulocyte colony stimulating factor WHIM 

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Copyright information

© Springer Nature Switzerland AG 2019

Authors and Affiliations

  • Mihaela Tatiana Bataneant
    • 1
    • 2
  1. 1.“Victor Babes” University of Medicine and PharmacyTimisoaraRomania
  2. 2.“Louis Turcanu” Children’s Emergency Clinical HospitalTimisoaraRomania

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