Cervical Lymphadenitis

  • Laura Marques
  • Lidia Branco
  • Julia Vasconcelos
  • Esmeralda Neves


Chronic granulomatous disease (CGD) is caused by a defect in phagocytes NADPH oxidase complex that is responsible for the phagocytes respiratory burst

The screening diagnostic test is the oxidative burst test

Patients with X-linked forms usually present in the first years of life but autosomal recessive forms may present later and be milder

The first-line curative treatment in CGD is hematopoietic stem cell transplantation


Chronic granulomatous disease NADPH oxidase Oxidative burst test Leishmania donovani Kala Azar 


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Copyright information

© Springer Nature Switzerland AG 2019

Authors and Affiliations

  • Laura Marques
    • 1
  • Lidia Branco
    • 2
  • Julia Vasconcelos
    • 2
  • Esmeralda Neves
    • 2
    • 3
  1. 1.Paediatric Infectious Diseases and Immunodeficiencies Unit, Centro Materno-Infantil do Norte, Centro Hospitalar do PortoPortoPortugal
  2. 2.Immunology DepartmentCentro Hospitalar do PortoPortoPortugal
  3. 3.Network of Immunity in Infection, Malignancy and Autoimmunity (NIIMA), Universal Scientific Education and Research Network (USERN)PortoPortugal

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