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Treacher Collins-Franceschetti Syndrome

  • Patricia Cecchi
  • Darina Krastinova
Chapter

Abstract

The most typical feature of Treacher Collins-Franceschetti syndrome is the antimongoloid slant of the palpebral fissures. This is due to absence or hypoplasia of the zygomatic-malar buttress and ectropion of the lower lid. Reconstruction with cranial bone grafts, upper lid flaps, and lateral canthopexy consents progressive normalization of facial features.

Keywords

Treacher Collins-Franceschetti syndrome Craniofacial surgery Lid reconstruction 

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Copyright information

© Springer Nature Switzerland AG 2019

Authors and Affiliations

  • Patricia Cecchi
    • 1
  • Darina Krastinova
    • 2
  1. 1.Bambino Gesu Hospital, Plastic Surgery UnitRomeItaly
  2. 2.Clinique Chateaux de la MayeParisFrance

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