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Pleuroparenchymal Fibroelastosis

  • Maria Cecilia Mengoli
  • Thomas Colby
  • Alessandra Dubini
  • Giulio Rossi
  • Alberto Cavazza
Chapter

Abstract

Pleuroparenchymal fibroelastosis (PPFE) is a rare and possibly underrecognized idiopathic interstitial pneumonia, as defined by the updated 2013 ATS/ERS Classification. Here we present an emblematic case of pleuroparenchymal fibroelastosis and a detailed description of its clinical, radiological, and histopathological presentation.

Keywords

Pleuroparenchymal fibroelastosis Transbronchial cryobiopsy Diagnosis 

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Copyright information

© Springer Nature Switzerland AG 2019

Authors and Affiliations

  • Maria Cecilia Mengoli
    • 1
  • Thomas Colby
    • 2
  • Alessandra Dubini
    • 3
  • Giulio Rossi
    • 4
  • Alberto Cavazza
    • 1
  1. 1.Anatomia PatologicaAzienda Unità Sanitaria Locale-IRCCS di Reggio EmiliaReggio EmiliaItaly
  2. 2.Department of Laboratory Medicine and PathologyMayo Clinic ScottsdaleScottsdaleUSA
  3. 3.Department of Pathology, Operative Unit of Pathologic AnatomyAzienda USL della Romagna, Ospedale GB Morgagni-L PierantoniForlìItaly
  4. 4.Operative Unit of Pathologic AnatomyHospital St. Maria delle Croci, Azienda USL della RomagnaRavennaItaly

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