Orbital Retinoblastoma: Diagnosis and Management

  • Bhavna Chawla
  • Maya Hada


Orbital retinoblastoma is a potentially fatal disease. It is more prevalent in the developing world where delay in presentation and lack of access to healthcare contribute to poor survival rates. However, with the evolution of a multimodal therapy, the prognosis for survival has improved significantly. The current treatment protocols use a combination of high-dose systemic chemotherapy, followed by appropriate surgery, radiotherapy, and adjuvant chemotherapy. This chapter discusses in detail the clinical spectrum of orbital retinoblastoma, classification and subtypes, evaluation and investigations, strategies for management, and future perspectives.


Retinoblastoma Orbital Management 


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Copyright information

© Springer Nature Switzerland AG 2019

Authors and Affiliations

  • Bhavna Chawla
    • 1
  • Maya Hada
    • 2
  1. 1.Ocular Oncology Service Dr. Rajendra Prasad Centre for Ophthalmic SciencesNew DelhiIndia
  2. 2.Department of OphthalmologySMS Medical College & HospitalJaipurIndia

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